Academy of Medical Sciences of I.R. Iran Archives of Iranian Medicine 1029-2977 25 7 2022 07 01 Silhouette Lymphangioma: An Unknown Macular Form of Cutaneous Lymphangioma 456 459 10.34172/aim.2022.75 EN Betul Tas https://orcid.org/0000-0001-5378-1478 Seyda Andac Aysel Caglar Journal Article 10.34172/aim.2022.75 2021 02 21 2021 07 18 Unusual angiomatous or lymphangiomatous vascular malformations are rarely seen. One of them is lymphangioma (LA), which is a rare benign lymphovascular abnormality. LA is usually seen in the types of circumscriptum (or capillary), cavernous and cystic. Here, we report a unique case of LA with a patchy appearance. The patient presented due to unusual symptoms and eccentric clinical manifestation of the lesion. Here, we present a new lymphatic entity which was diagnosed as LA with its clinical, radiological and pathological findings. Written informed consent of the patient was obtained for this report. To the best of our knowledge this macular form of cutaneous LA has not been previously reported in literature. Macular LA should be kept in mind when faced with a colored long-term macular lesion on the skin.